Fibromatosis

Fibromatosis

Infobox_Disease
Name = PAGENAME


Caption =
DiseasesDB =
ICD10 = ICD10|M|72|9|m|70
ICD9 =
ICDO =
OMIM =
MedlinePlus =
eMedicineSubj =
eMedicineTopic =
MeshID = D005350
The term fibromatosis refers to a group of benign soft tissue tumors (fibromas) [DorlandsDict|three/000040062|fibromatosis] which have certain characteristics in common, including absence of cytologic and clinical malignant features, a histology consistent with proliferation of well-differentiated fibroblasts, an infiltrative growth pattern, and aggressive clinical behavior with frequent local recurrence.

Terminology

Other names include "musculoaponeurotic fibromatosis," referring to the tendency of these tumors to be adjacent to and infiltrating deep skeletal muscle, and "desmoid tumor," an obsolete term which more specifically refers to the occurrence of these tumors in the abdominal wall of a pregnant woman.

Fibromatosis is a different entity from neurofibromatosis.

Treatment

Treatment includes prompt radical excision with a wide margin and/or radiation. Despite the local infiltrative and aggressive behavior of these tumors, mortality secondary to these tumors is minimal to nonexistent.

ubtypes

Subtypes of fibromatosis include -
*juvenile fibromatosis
*fibromatosis colli
*infantile digital fibromatosis
*infantile myofibromatosis
*ipofibromatosis
*fibromatosis hyalinica multiplex
*plantar fibromatosis
*penile fibromatosis (Peyronie's disease)
*palmar fibromatosis (Dupuytren's contracture).

Associated conditions

Multiple fibromatoses are seen in Gardner's syndrome, a syndrome which also includes multiple colon polyps and osteomas.

References

*
* [http://www.maxillofacialcenter.com/BondBook/softtissue/fibromatosis.html maxillofacialcenter]
* Rosai, J. "Rosai and Ackerman's Surgical Pathology". Mosby Inc., 2004. pg 2249-2252.


Wikimedia Foundation. 2010.

Игры ⚽ Поможем написать курсовую

Look at other dictionaries:

  • fibromatosis — f. oncol. Formación de fibromas, especialmente en la piel y en el útero. Tras la extirpación suelen reaparecer pero nunca ocasionan metástasis. Medical Dictionary. 2011. fibromatosis …   Diccionario médico

  • fibromatosis — ► sustantivo femenino MEDICINA Aumento circunscrito de tejido conjuntivo rico en fibras. IRREG. plural fibromatosis …   Enciclopedia Universal

  • fibromatosis gingival — crecimiento fibroso excesivo difuso del tejido gingival. En la forma generalizada hay exceso de tejido en ambos maxilares, que puede transmitirse como carácter autosómico dominante, ser producido por drogas, especialmente anticonvulsivos como… …   Diccionario médico

  • fibromatosis seudosarcomatosa — nódulo tumoral subcutáneo poco común de superficie dura y firme gris a rosada, que puede aparecer en cualquier parte del cuerpo incluso labios y cavidad bucal. La lesión, parecida histológicamente al fibrosarcoma, se compone de células de tejido… …   Diccionario médico

  • fibromatosis gingivae — gingival fibromatosis 1. generalized or localized diffuse fibrous overgrowth of the gingival tissue, usually transmitted as an autosomal dominant trait, but some cases are idiopathic and others produced by drugs (see Dilantin gingivitis, under… …   Medical dictionary

  • fibromatosis — 1. A condition characterized by multiple fibromas, with relatively widespread distribution. 2. Abnormal hyperplasia of fibrous tissue. abdominal f. SYN: desmoid (2). aggressive in …   Medical dictionary

  • fibromatosis — fi·bro·ma·to·sis …   English syllables

  • fibromatosis — A condition in which multiple fibromas develop. Fibromas are tumors (usually benign) that affect connective tissue …   English dictionary of cancer terms

  • fibromatosis — …   Useful english dictionary

  • palmar fibromatosis — fibromatosis involving the palmar fascia, and resulting in Dupuytren contracture …   Medical dictionary

Share the article and excerpts

Direct link
Do a right-click on the link above
and select “Copy Link”